Abstract
Adrenocortical carcinoma – 12-year observation period in a single centre. Case report with literature review
- Department of Endocrinology, Children's Memorial Health Institute, Warsaw, Poland
- Department of Oncology, Children's Memorial Health Institute, Warsaw, Poland
- Department of Surgery, Children's Memorial Health Institute, Warsaw, Poland
- Department of Pathology, Children's Memorial Health Institute, Warsaw, Poland
Background
Adrenocortical carcinoma (ACC) accounts for 0.2% of childhood malignancies. The most common symptom in children is rapidly progressive androgenization. Herein, we report a case of a patient with symptoms of hypercortisolaemia and androgenization, who was diagnosed with ACC.
Case presentation
In a 10-year-old patient with ACC the course of the disease was complicated by 3 recurrences. She was treated with surgery, chemo-, and radiotherapy. Currently, 8 years after the end of treatment, there have been no signs of recurrence.
Conclusions
A patient after ACC treatment requires regular check-ups and long-term observation. Constant supervision enables early diagnosis of disease recurrence, and the use of treatment improves the prognosis.
Keywords
adrenocortical carcinoma, adrenocortical tumour, mitotan
Integrated with
