Facial nerve schwannoma (neurilemmoma – FNS) is a benign, slowly growing tumor arising from the Schwann cells of the facial nerve sheath. Its most common symptom is progressive facial nerve palsy, but if it develops in the intratemporal region, it may also cause unilateral hearing loss. Another, much less common neoplasm that develops in the temporal bone is the endolymphatic sac tumor (ELST). In some cases of this tumor, facial nerve palsy is also observed, but dominant symptom of this tumor is unilateral, progressive hearing loss. Imaging play an important role in differentiating both neoplasms. This article presents a description of a 67-year-old patient operated on for a facial schwannoma, who was referred to a clinic with suspected endolymphatic sac tumor.