@Article{Czopek2013,
journal="Folia Neuropathologica",
issn="1641-4640",
volume="51",
number="2",
year="2013",
title="Case reportEndolymphatic sac tumour (ELST). Case report of a rare tumour of the temporal bone, presenting as a mass in a cerebello-pontine angle",
abstract=" Endolymphatic sac tumour (ELST) is a primary low-grade, locally invasive adenocarcinoma of the endolymphatic sac, charac-  terized by the proliferation of cuboidal cells forming a papillotubular pattern and colloid-filled cysts. Rare in the general population, it coincides significantly with the presence of von Hippel-Lindau disease. The natural history, mechanisms underlying the early symptoms, anatomical origin of ELST and optimal timing of their treatment are unknown. In this study, we report a Polish male patient with sporadic ELST (without a family history of VHL disease) along with a review of literature. The light microscopic and immunohistochemical features as well as clinical presentation were typical of ELST. ",
author="Czopek, Jacek
and Waśko, Marcin
and Adamek, Dariusz",
pages="164--168",
doi="10.5114/fn.2013.35960",
url="http://dx.doi.org/10.5114/fn.2013.35960"
}