TY - JOUR JO - Pediatric Endocrinology Diabetes and Metabolism SN - 2081-237X VL - 26 IS - 3 PY - 2020 ID - Attri2020 TI - Cushing’s syndrome due to primary pigmented nodular adrenal disease in two brothers with Carney complex AB - Two brothers (19 and 18 years old, respectively) presented with weight gain and stunted growth since the age of 10 years. They had spotty skin pigmentation over the face along with florid features of Cushing’s syndrome with low bone density, renal calculi, dyslipidaemia, hypertension, and dilated cardiomyopathy. They underwent evaluation of the hypothalamic-pituitary-adrenals axis, which suggested ACTH-independent Cushing’s syndrome, and the abdominal CT imaging revealed normal adrenals. The diagnosis of Familial Cushing’s syndrome with primary pigmented nodular adrenal disease and Carney complex was made. Bilateral adrenalectomy was carried out in both of them with resolution of the features of hypercortisolaemia post-operatively. AU - Attri, Bhawna AU - Aggarwal, Anshita AU - Mattoo, Sahil AU - Kulshreshtha, Bindu SP - 155 EP - 158 DA - 2020 DO - 10.5114/pedm.2020.95625 UR - http://dx.doi.org/10.5114/pedm.2020.95625 ER -