Introduction

Folliculotropic mycosis fungoides is one of the mycosis fungoides variants with neoplastic T-helper lymphocytes infiltrating hair follicles. It often affects head and neck with a variety of lesions.

Objective

To present a patient with folliculotropic mycosis fungoides and coexisting pancreatic neuroendocrine tumour.

Case report

A 63-year-old male with a 15-year history of erythematous-papular exfoliating lesions with pruritus has been treated in ambulatory care. After 10 years he was referred to the hospital. Lesional biopsy was non-specific at that time. Five years later folliculotropic mycosis fungoides was diagnosed on the basis of clinical and histopathological features. The patient underwent Re-PUVA therapy with no improvement, and then methotrexate was introduced. At that time the diagnosis of coexisting pancreatic neuroendocrine tumour was made.

Conclusions

Folliculotropic mycosis fungoides is a rare type of cutaneous T-cell lymphoma with a 5-year survival rate reaching 80%. The presented case highlights the possibility of atypical clinical features of the diseases and coexistence of other neoplastic comorbidities.