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eISSN: 2449-6731
ISSN: 2449-6723
Prenatal Cardiology
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1/2019
 
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abstract:
Case report

Prenatal diagnosis of fetal cardiac rhabdomyoma with severe cardiac dysfunction

Luciane Alves da Rocha Amorim
1, 2
,
Denilson de Souza Veras
1
,
Edward Araujo Júnior
2

1.
Postgraduate Program in Health Sciences, Medical School, Federal University of Amazonas (UFAM), Manaus, Brazil
2.
Department of Obstetrics, Paulista School of Medicine, Federal University of São Paulo (EPM-UNIFESP), São Paulo, Brazil
Prenat Cardio 2019; 9(1): 47-50
Online publish date: 2020/01/22
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Fetal cardiac tumours are rare, but rhabdomyomas are the most common. They are associated with tuberous sclerosis in 50–80% of cases. Early diagnosis of cardiac rhabdomyoma is thus important for early diagnosis of tuberous sclerosis. We describe a case of an intracardiac tumour that evolved with significant ventricular dysfunction. The report of this case teaches us an important lesson by exemplifying an unsuccessful experience of rhabdomyoma surgery.
keywords:

prenatal diagnosis, fetal cardiac tumour, rhabdomyoma, cardiac dysfunction

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