eISSN: 2300-8660
ISSN: 0031-3939
Pediatria Polska - Polish Journal of Paediatrics
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vol. 96
Review paper

Vomiting, constipation, and abdominal pain during menstruation as first symptoms of Herlyn-Werner-Wunderlich syndrome: case report and literature review

Justyna Konys
1, 2
Jakub M. Kucharski
1, 2
Barbara Skowrońska
Aleksandra Banaszkiewicz
Marcin Banasiuk

  1. Students’ Scientific Group GEKON, Department of Pediatric Gastroenterology and Nutrition, Medical University of Warsaw, Poland
  2. Department of Pediatric Gastroenterology and Nutrition, Medical University of Warsaw, Poland
Pediatr Pol 2021; 96 (3): 213–216
Online publish date: 2021/09/29
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Herlyn-Werner-Wunderlich syndrome, also known as OHVIRA (Obstructed Hemivagina and Ipsilateral Renal Anomaly), is an extremely rare abnormality of the Müllerian ducts, characterized by the presence of double uterus, unilateral cervico-vaginal obstruction and renal agenesis and/or other urinary tract anomalies. Most cases are diagnosed after menarche through an MRI, CT or ultrasound. There are no specific symptoms of this syndrome. Patients presented fever and vomiting during menstruation, intermenstrual bleeding and palpable abdominal, pelvic or vaginal mass. Thorough history taking is extremely important as common symptoms in pediatrics (vomiting, constipation, abdominal pain) may be a part of a more complex condition, not only within the GI tract but also including other systems.

constipation, children, didelphys uterus, hematometrocolpos, renal agenesis