Introduction. Rowell’s syndrome is a rare subtype of subacute lupus erythematosus associated with erythema multiforme-like skin lesions, positive antinuclear antibodies and anti-Ro/La-antibodies.

Objective. To present a case of Rowell’s syndrome.

Case report. We describe a case of an 82-year-old man who presented with erythema multiforme-like eruption on the upper extremities and trunk and fulfilled the diagnostic criteria of Rowell,s syndrome.

Conclusions. Patients with these characteristic clinical and immunological features of Rowell,s syndrome are rarely seen and reported in the literature. The discussion concerning the character of the disease is still ongoing.