Kardiochirurgia i Torakochirurgia Polska

Abstract

2/2015 vol. 12

CASE REPORTS
Potts’ shunt in a child with idiopathic pulmonary arterial hypertension – one-and-a-half year observation

Kardiochirurgia i Torakochirurgia Polska 2015; 12 (2): 170-172
Online publish date: 2015/07/10
View full text
Confronting perimenopausal women’s knowledge of coronary heart disease with their health behaviours. Controversial role of hormone replacement therapy in the protection of coronary heart disease
This paper presents the case of a young girl with idiopathic pulmonary hypertension, who developed signs of severe heart failure within a short period of time. Pharmacotherapy with sildenafil and bosentan (among other drugs) was ineffective. Heart catheterization revealed suprasystemic pressure in the pulmonary artery. At the age of 7.5 years, the patient underwent a surgical Potts shunt (namely, a direct side-by-side anastomosis from the left pulmonary artery to the descending aorta). The procedure resulted in a significant improvement of the clinical, echocardiographic, and biochemical parameters, which persists after one and a half years of follow-up. After the surgery, pharmacotherapy with bosentan was gradually discontinued.
Share
without publication fees
without publication fees