|
Current issue
Archive
Manuscripts accepted
About the journal
Editorial board
Abstracting and indexing
Contact
Instructions for authors
Ethical standards and procedures
Editorial System
Submit your Manuscript
 
|
5/2019
vol. 94 abstract:
Case report
A rare case of mediastinal fibromatosis in a child – case report
Dorota Aleksandra Nadbrzeżna
1
,
Aleksandra Raźnikiewicz
2
,
Andrzej Grabowski
2
,
Wojciech Korlacki
2
,
Tomasz Szczepański
3
,
Joanna Bulsa
3
,
Małgorzata Walaszczyk
4
1.
Department of General Surgery, Municipal Hospital Complex in Chorzow, Poland
2.
Department of Children’s Developmental Defects Surgery and Traumatology, School of Medicine with the Division of Dentistry in Zabrze, Medical University of Silesia in Katowice, Zabrze, Poland
3.
Department of Paediatric Haematology and Oncology, School of Medicine with the Division of Dentistry in Zabrze, Medical University of Silesia in Katowice, Zabrze, Poland
4.
Department of Anaesthesiology and Intensive Therapy, School of Medicine with the Division of Dentistry in Zabrze, Medical University of Silesia in Katowice, Zabrze, Poland
Pediatr Pol 2019; 94 (5): 328–331
Online publish date: 2019/11/19
View full text
Get citation
ENW EndNote
BIB JabRef, Mendeley
RIS Papers, Reference Manager, RefWorks, Zotero
AMA
APA
Chicago
Harvard
MLA
Vancouver
Introduction
Fibromatosis is a very rare desmoid tumour. It is characterised by local invasion and infiltration of close structures. The treatment is mainly surgical. Material and methods We report the case of 1.5-year-old boy admitted to the Paediatric Hospital, with a diagnosis of mediastinal desmoid fibromatosis. He was treated surgically (thoracoscopy and thoracotomy), chemotherapy was used, and he was hospitalised in the Intensive Care Unit more than once. Despite intensive treatment, the patient perished. Results and conclusions Fibromatosis is classified as a desmoid tumour. Rare tumour localisation and invasive tumour characteristics causes considerable difficulty in the diagnosis, despite the use of many diagnostic methods. keywords:
thoracotomy, mediastinum, fibromatosis, desmoid tumour |
POLSKI
