eISSN: 1897-4309
ISSN: 1428-2526
Contemporary Oncology/Współczesna Onkologia
Current issue Archive Manuscripts accepted About the journal Supplements Addendum Special Issues Abstracting and indexing Subscription Contact Instructions for authors
SCImago Journal & Country Rank
2/2018
vol. 22
 
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abstract:
Case report

Giant cranionasal epithelioid haemangioendothelioma with invasive growth pattern mimicking a skull base chondrosarcoma

Kelvin Piña Batista
,
Gonzalo Lepe Gómez
,
Eduardo Murias Quintana
,
Aurora Astudillo
,
Ivan Fernandez-Vega
,
Belen Alvarez Fernandez
,
Ana Cuellar-Martínez
,
José Llorente-Pendás
,
Veronica Rovira-Pereira
,
Kenia Alvarez-Reyes

Contemp Oncol (Pozn) 2018; 22 (2): 118-123
Online publish date: 2018/06/13
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Epithelioid haemangioendothelioma (EHE) is a rare low-grade vascular neoplasm that is composed of mostly epithelioid cells. EHE may arise as a solitary tumour or in the form of multiple body lesions, and commonly occurs in soft tissues, liver, pleura, lung, peritoneum, lymph nodes, breast, and many other sites. EHE in the cranionasal region is extremely rare. There are very few reports of cases of skull-base EHE. We discuss an extremely rare presentation of an aggressive EHE that originated from the sellar region. Based on literature review, our patient is the first reported case of a giant solitary EHE with prepontine cistern invasion and abducens nerve encroachment mimicking a chondrosarcoma. We treated this rare tumour by near subtotal surgical excision with subsequent radiotherapy, considering that complete tumour resection with free margins in both cavernous sinus and clival region avoiding neural and vascular structure encroachment becomes technically difficult.
keywords:

epithelioid haemangioendothelioma, vascular tumour, skull base, cranionasal

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