eISSN: 1897-4309
ISSN: 1428-2526
Contemporary Oncology/Współczesna Onkologia
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vol. 22
Case report

Rosette-forming glioneuronal tumour of the fourth ventricle. Not always a foreseeable development

Aida Antuńa Ramos, Ivan Fernandez Vega, Kelvin Pińa Batista, Vanesa Martin Fernandez, Carmen Rodriguez Sanchez, Marco Antonio Alvarez Vega

Contemp Oncol (Pozn) 2018; 22 (4): 270-274
Online publish date: 2018/12/31
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Aim of the study
Rosette-forming glioneuronal tumour (RGNT) of the fourth ventricle is an uncommon tumour. The management is not consensual. Most of the published cases show stable outcome with and without gross total resection and are regarded as having a relatively indolent behaviour.

Material and methods
We present a 32-year-old man with a tumour in the fourth ventricle. He underwent midline suboccipital craniectomy with gross total removal.

The histopathological diagnosis was RGNT grade I. Four years later he presented a radiological progression and received stereotactic radiosurgery. At the last follow-up seven years after surgery, the MRI showed no recurrence.

RGNT should be considered in the differential diagnosis of a posterior fossa tumour and has to be differentiated from other lesions for its indolent course and favourable prognosis. Surgical procedures should be carefully performed to avoid serious surgical morbidities. Stereotactic radiosurgery treatment appears to be a useful treatment in recurrence episodes.


Rosette-forming glioneuronal tumour, fourth ventricle, posterior fossa, radiosurgery

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