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eISSN: 2300 - 8660
ISSN: 0031-3939
Pediatria Polska - Polish Journal of Paediatrics
Bieżący numer Archiwum Artykuły zaakceptowane O czasopiśmie Rada naukowa Bazy indeksacyjne Kontakt Zasady publikacji prac
SCImago Journal & Country Rank

 
2/2022
vol. 97
 
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Opis przypadku

Management of the local relapse of the bladder – prostate rhabdomyosarcoma

Marcelina Spychała
1
,
Grzegorz Maroszek
1
,
Agata Maria Kawalec
2, 3
,
Jan Godziński
2, 4

1.
Students’ Scientific Association, Wroclaw Medical University, Wroclaw, Poland
2.
Department of Paediatric Surgery, Marciniak Hospital, Wroclaw, Poland
3.
Department of Human Biology, University of Wroclaw, Wroclaw, Poland
4.
Department of Emergency and Disaster Medicine, Wroclaw Medical University, Wroclaw, Poland
Pediatr Pol 2022; 97 (2): 159-164
Data publikacji online: 2022/06/20
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Introduction
Rhabdomyosarcoma (RMS) is the most common soft-tissue sarcoma in children. Genitourinary locations occur in approximately 20–30% of cases. Children with RMS localized in the bladder or/and prostate require multi-modal therapy with systemic chemotherapy in conjunction with surgery or radiation therapy to maximize local tumour control.

Case report
The report presents a case of a 3-year-old boy diagnosed in 2015 with embryonal RMS, who was treated due to relapse of RMS in the urinary bladder in 2016–2018. The patient was treated with chemotherapy, radiotherapy, and surgery (the urinary bladder was excised, and a neobladder was created according to Florida-pouch procedure). Currently, the patient is in the 3rd year of observation after the end of oncological treatment

Conclusions
The treatment for RMS localized in the bladder puts the priority on organ-sparing techniques. Radiotherapy or brachytherapy are standard supplementary treatments. However, in the case of relapse, mutilating rescue surgery still has value.

słowa kluczowe:

surgical treatment, bladder tumour, rhabdomyosarcoma