Autoimmune pancreatitis (AIP) is a rarely diagnosed systemic disease causing a number of dilemmas which result from vague diagnostic criteria and not simultaneously emerging symptoms. Imaging features of AIP often mimic pancreatic or biliary tract cancer, exposing patients to extensive and crippling surgery. The histological examination shows intense tissue fibrosis leading to the sclerosis of involved organs and immunohistochemistry reveals T-lymphocytic and plasmacytic infiltration with predominance of cells producing IgG4 subclass immunoglobulins. We present a case of a 50-year-old woman with 11 years history and multisymptomatic course of AIP who died from urologic complications